What is LQT

The Long QT syndrome is an abnormality of the hearts electrical system. The heart muscle is made up of millions of cells, each cell has pores in a membrane termed ion channels, these allow the movement of chemicals in and out of the cells providing the electrical signal generating the heart beat. The long QT syndrome is caused by a disorder of cells that affects the production of the electrical signal. This extends the QT interval which can normally be seen on an ECG trace. The extended QT interval delays the recovery of the heart muscle before the next beat.

The extended QT interval can be associated with arrhythmias causing rapid chaotic heart rhythms that lead to improper pumping of blood with resultant abrupt syncope.

The long QT syndrome may be inherited or it may be induced by some medications.

What are the symptoms of LQT?

Unexplained syncope (fainting ) especially during physical exertion or emotional stress although not all patients with LQT will suffer syncope.